OR roughness – a rare disorder with which the diagnosed the 15-year-old Dimitris from Metsovo- stood catalytic in the evolution and outcome of heat stroke suffered by the teenager last Thursday (24.07.2025).
According to what is known to 15 -year -old Dimitris is suffering from a rare developmental condition – Honestly – which prevents its body from sweating and regulating its temperature, which led him to collapse with acute liver failure, when he was found in severe heat during hiking.
The 15 -year -old hospitalized in a special center in Turin, Italyin order to undergo a liver transplant. Time battle is relentless for healthcare professionals as a compatible graft must be found as soon as possible, within the next 24 hours, to treat the thunderbolt hepatic insufficiency due to heat stroke.
But what is Honestly and how is it treated?
Honestly is a situation in which The sweat glands do not work as they should to remove heat and cool the body. Thus the body is overheated, which can be dangerous or even life -threatening.
It is not known how many people suffer from roughness. Many people with mild cases may not notice that they do not sweat or may not visit their doctor. Some people are born with this disorder, while others develop it later in their lives.
Indications that make up a bell
- Skin lesions from burns, radiotherapy or diseases that clog pores, such as psoriasis.
- Damages to the sweat glands from surgery, trauma or scarring.
- Nerve damage caused by diabetes, alcoholism and Guillain-Barre syndrome.
- Hereditary disorder of the metabolic system (Fabry disease).
- Connecting tissue disorders, such as systemic sclerosis, systemic lupus erythematosus, Sjogren syndrome.
- Autonomic nervous system disorders, such as ROSS syndrome and Harlequin syndrome.
- Nervous diseases (neuropathies), such as diabetes -related neuropathy, paraneoplastic neuropathy, hereditary neuropathy, amyloid neuropathy, leaky neuropathy.
- Diseases and diseases of the central nervous system, including multiple systemic atrophy, lewy body dementia, Parkinson’s disease, stroke and spinal cord disease.
- Excessive dehydration.
- Many medicines prevent the function of sweat glands.
- Anticholinergic drugs are the most common medicinal cause of roughness. Examples of anticholinergic drugs include glycopyrol, doxepine, atropine (Atropen®), cyproeptadine and yosycamine. Other categories of drugs and examples include: tricyclic antidepressants (amitripline), antihistamines, bladder anticonvulsions, antipsychotic / anti -emetic, anti -epileptic, antihypertensive, opioid, neuromuscular paralytic.
Symptoms of roughness
- Little or no sweating
- Dizziness
- Redness
- Muscle cramps
- General weakness
- Feeling hot and inability to cool
- You may have a loss of ability to sweat in specific areas of your body or loss of sweating may be general. Another motive of roughness is the lack of sweat or very limited sweating in specific areas of the body, but intense sweating in other areas. This is because your body is trying to offset the lack of sweat in one or more other areas of the body. Usually this is not dangerous because your body is still able to cool.
What should I do if I show symptoms of roughness
If you have symptoms, it is recommended to make an appointment with your doctor. Talk to him your inability to sweat and the other symptoms you have.
Your doctor will ask you questions about your inability to sweat. You may also be asked to undergo sweat test. In this testcover you with a dust that changes color to the points where you sweat. They take you to a chamber to sweat to see which parts of your body are sweating.
You may undergo skin biopsy to determine the presence of nerve fibers and determine the possible cause of roughness. You may undergo other exams to identify other underlying causes of rhythms.
If you have these symptoms in a warm environment, remove immediately from the heat and go to a shady place or indoors, preferably with air conditioning.
Relax your clothes and, if possible, place cool wet sails on your body. Ask for medical help if your symptoms do not improve as you get cold.
There are serious complications that may arise from roughness
Serious cases of roughness, where most of the or whole body does not sweat, can lead to serious heat -related diseases, such as:
Thermal exhaustion: Signs and symptoms are weakness, nausea, tachycardia after intense activity in warm weather. Treatments include moving to a cooler place, water consumption, cool compresses or taking a cool shower.
Heat stroke: This is an extremely dangerous, life -threatening condition at which body temperature rises to 39.4 ° C or more. Heating can cause confusion, loss of consciousness, coma and even death. Call 166 or carry the person to the hospital. Move the person to a shady place, remove unnecessary clothes and cool it (use ice cream, cold water sponge, apply cool wet towels, spray its body with water).
If roughly is caused by a medicine, It can be reversible if you stop taking the drug. Do not stop taking the drug without first consulting your doctor. If humanity is caused by a medical condition, this condition may be treatable. If no other medical cause is identified, the treatment of rhymes may be limited to avoiding situations where deficiency is causing health problem, such as heat -related diseases.
What can I expect if I have roughness
Humanity is usually a disorder that lasts all life. However, the prognosis depends on whether the underlying cause can be found and whether the cause is treatable. Treatment of underlying medical condition should improve roughness. If humanity is caused by a medicine, it is usually reversible when the drug is discontinued.
The most significantly things you can do if you have been diagnosed with roughness is as follows:
- Keep your body cool while staying in a cool environment.
- Don’t overwhelm yourself.
- Take precautions when you are outdoors in warm climates (prevention).
- Learn the signs and symptoms of heat exhaustion and heat stroke and find out what to do if they appear.
When should I see a doctor
If you notice that you do not sweat at all or sweat too little on hot days or during activities that would normally cause sweating.
If you notice that you sweat a little, you sweat less than usual (hypodrosis) or do not sweat at all.
Require medical help immediately if you have signs or symptoms of heat stroke.
Can it be prevented?
Humanity cannot be prevented, but you can do some things to avoid overheating, such as:
- Wear wide, light -colored clothes and hat with wide cornice.
- Stay in a cool (air -conditioned) place or move in the shade.
- To take a cool shower or sit in a bathroom with cool water.
- Stay hydrated. Drink a lot of liquids, special water or sports drinks. Do not drink alcohol or drinks containing caffeine (coffee, tea, cola, chocolate).
- Slowly move, do not overly strain yourself, do not do intense exercise.
- Have a bottle of water with you wherever you go. You can drink water or, in case of emergency, use it to cool your body if you are out and you cannot move to a cooler place.
Source: iatropedia.gr